In its place there was a small depression, a prenasal fossa in the lower margin of the nasal vestibule. The first description of maxillonasal dysplasia goes back to 1882 when Zuckerkandl 3 described an anomaly of the nasal fossa floor in which the normal crest that separates the nasal floor from the anterior surface of the maxillary bone was absent. Noyes 2 described the clinical features of maxillonasal dysplasia before Binder, but he did not recognize it as a syndrome. Before 1962, the few cases described of this malformation were identified in scientific publications with other names such as "facies scaphoidea", "flat face" or "congenitally flat nose syndrome" 1 In 1962, Binder described three children with the following characteristics: maxillonasal hypoplasia, convex upper lip, vertical nose, flat nasofrontal angle, absence of an anterior nasal spine, atrophy of the nasal mucosa, and hypoplasia of the frontal sinuses. Palabras clave: Displasia maxilo-nasal Síndrome de Binder Injerto de cartílago costal.īinder syndrome is a congenital pathology characterized by a failure in the development of the premaxilla. En este trabajo hemos realizado una revision bibliográfica sobre la etiología, el diagnóstico diferential y el tratamiento de la sindrome de Binder y presentamos un caso clínico de un paciente binderiano sometido a intervención de cirugía ortognática y rinoplastia con injerto de cartílago costal para recostruir el dorso y la punta nasal. El tratamiento del los pacientes con síndome de Binder puede ser ortodóntico o quirúrgico según la gravedad de la malformación.
Key words: Maxillonasal dysplasia Binder syndrome Rib cartilage graft.Įl síndrome de Binder es una patología caracterizada por hipoplasia nariz-maxilar, ángulo naso-frontal plano, senos frontales hipoplasicos, ausencia de la espina nasal anterior, columela corta y ángulo nasolabial agudo. We present the case of a boy with this syndrome surgically treated with orthognatic surgery and rhinoplasty with an L-shaped rib cartilage graft. We review the literature on the etiology, differential diagnosis and treatment of Binder syndrome. The patient can be treated orthodontically or surgically depending on the seriousness of the malformation. University of Rome "La Sapienza", Roma, Italiaīinder syndrome is a disorder characterized by nasomaxillary hypoplasia that results in a short nose, a frontonasal angle of almost 180 degrees, hypoplasia of the frontal sinuses, an absent anterior nasal spine, a short columella and an acute nasolabial angle. Orthognathic surgery and rhinoplasty in Binder syndromeĬirugía ortognática y rinoplastia en el síndrome de Binderĭepartment of Maxillo-Facial Surgery.